3-Hydroxyisovalerylcarnitine, CAS 99159-87-2

Description: 3-Hydroxyisovalerylcarnitine is a carnitine derivative that may serve as a novel biomarker for biotin deficiency in humans, with its concentration increasing in such conditions. Biotin deficiency reduces the activity of biotin-dependent 3-methylcrotonyl-CoA carboxylase, hindering the conversion of 3-methylcrotonyl-CoA into 3-methylglutaconyl-CoA, and impairing the leucine catabolism pathway, resulting in elevated plasma 3-Hydroxyisovalerylcarnitine concentrations [1].

CAS Number: 99159-87-2

Formula: C12H23NO5

Molecular Weight: 261,31

• SKU: TGMTN7605-10mg
• Manufacturer: TargetMol Chemicals
• Manufacturer SKU: TN7605-10mg
• Package Unit: 10 mg
• Quantity Unit: STK