Shelf life (days): 1460.0
Formulation: A solid
Purity: ≥95%
Formula Markup: C8H15NO3
Formula Weight: 173.20964
CAS Number: 3077-46-1
Notes: N-acetyl-L-Isoleucine is an acetylated form of L-isoleucine. Urine levels of N-acetyl-L-isoleucine are increased in patients with maple syrup urine disease (MSUD), an inborn error of metabolism characterized by a deficiency in the branched-chain α-ketoacid dehydrogenase complex, the complex that catalyzes the degradation of branched-chain amino acids, leading to the accumulation of branched-chain amino acids in the plasma and urine, a maple syrup-like odor in the urine, and neurological impairments.{57731}